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阵发性睡眠性血红蛋白尿症
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阵发性睡眠性血红蛋白尿症
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医学
造血干细胞移植
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paroxysmal nocturnal hemoglobinuria
阵发性睡眠性血红蛋白尿症
后天获得性造血干细胞磷脂酰肌醇糖苷-A(PIG-A)基因突变引起的红细胞膜缺陷性溶血性疾病。简称PNH。
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