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单词
X-linked agammaglobulinemia,XLA
释义
X-linked agammaglobulinemia,XLA
Encyclopedia
医学
原发性B细胞缺陷
释
X-linked agammaglobulinemia,XLA
X连锁无丙种球蛋白血症
在B细胞分化成熟的早期,X染色体上Bruton酪氨酸激酶(Btk)基因突变或缺失,使前B细胞信号转导受阻,分化和成熟发生障碍,不能合成免疫球蛋白的原发性B细胞免疫缺陷病。又称布鲁顿无丙种球蛋白血症、Bruton病。是最常见的以抗体缺陷为主的原发性免疫缺陷病。
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linearization principle
linearization theorem
linearized augmented plane wave
linearized augmented plane wave, LAPW
linearized augmented plane wave method
linearized augmented plane wave method, LAPW method
linearized augmented plane waves
linearized augmented plane waves (LAPW)
linearized Boltzmann equation
linearized collision integral
linearized collisionless Boltzmann equation
linearized collision operator
linearized cone
linearized Einstein equation
linearized equation
linearized equations of motion
linearized models for energy band calculation
linearized muffin tin orbital method
linearized muffin-tin orbital method
linearized muffin tin orbital method, LMTO method
linearized operator
linearized semi classical initial value representation
linearized semi-classical initial value representation
linearized stability analysis
linearized system
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