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Fabry disease
释义
Fabry disease
Encyclopedia
医学
法布里病
释
Fabry disease
法布里病
X染色体连锁隐性遗传的先天性糖鞘磷脂代谢异常的疾病。是由细胞溶酶体内α-半乳糖苷酶先天性活性降低或缺乏导致的代谢性疾病。又称α-半乳糖苷酶缺乏症。
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airworthiness
airworthiness approval
airworthiness certification
airworthiness certification flight test
airworthiness compliance verification
airworthiness design approval
airworthiness design assurance system
airworthiness design compliance
airworthiness directives
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airworthiness noise test
airworthiness of aircraft
airworthiness production approval
airworthiness regulation
airworthiness regulations
airworthiness status of civil aircraft
Airy
airy
Airy crater
Airy differential equation
Airy diffraction pattern
Airy disk
Airy-Fock function
Airy function
Airy-Heiskanen isostatic model
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